A rare case of sporadic supratentorial hemangioblastoma
https://doi.org/10.35401/2500-0268-2020-18-2-57-63
Abstract
We report the rare case of 65-year-old male patient with supratentorial hemangioblastoma and gigantic cyst of the left hemisphere of the brain without von Hippel-Lindau disease. Hemangioblastoma is a rare benign tumor classified as grade I by the WHO of the central nervous system of uncertain histogenesis. This neoplasm’s stroma consists of dense networks of thin-walled blood vessels of various calibers. About 140 cases of supratentorial localization of this type of tumor are presented in the world literature. We have given a fairly complete clinical, neuroradiological and histological picture that allows one to differentiate hemangioblastoma from other histological structures. Promising modalities in the treatment of patients with this pathology when it is impossible to perform total tumor resection are considered.
About the Authors
V. E. Kocharyan
Scientific Research Institute – Ochapovsky Regional Clinical Hospital no. 1;
Kuban State Medical University
Russian Federation
Russian Federation
Vladimir E. Kocharyan, Neurosurgeon, Neurosurgery Department no. 1; Postgraduate Student, Department of Nervous Diseases and Neurosurgery, Faculty of Advanced Training and Professional Retraining of Specialists
167, 1st May str., Krasnodar, 350086
T. G. Sarkisyan
Scientific Research Institute – Ochapovsky Regional Clinical Hospital no. 1;
Kuban State Medical University
Russian Federation
Russian Federation
Tigran G. Sarkisyan, Neurosurgeon, Neurosurgery Department no. 1; Postgraduate Student, Department of Nervous Diseases and Neurosurgery, Faculty of Advanced Training and Professional Retraining of Specialists
G. I. Kovalev
Scientific Research Institute – Ochapovsky Regional Clinical Hospital no. 1
Russian Federation
Russian Federation
Georgy I. Kovalev, Cand. of Sci. (Med.), Head of the Neurosurgery Department no. 1
G. G. Muzlaev
Scientific Research Institute – Ochapovsky Regional Clinical Hospital no. 1;
Kuban State Medical University
Russian Federation
Russian Federation
Gerasim G. Muzlaev, Neurosurgeon, Neurosurgery Department no. 1; Dr. of Sci. (Med.), Professor, Head of the Department of Nervous Diseases and Neurosurgery, Faculty of Advanced Training and Professional Retraining of Specialists
A. I. Bogrov
Kuban State Medical University
Russian Federation
Russian Federation
Andrey I. Bogrov, Sixth-Year Student of the Pediatric Faculty
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Review
For citations:
Kocharyan V.E., Sarkisyan T.G., Kovalev G.I., Muzlaev G.G., Bogrov A.I. A rare case of sporadic supratentorial hemangioblastoma. Innovative Medicine of Kuban. 2020;(2):57-63. (In Russ.) https://doi.org/10.35401/2500-0268-2020-18-2-57-63
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